Haematologica
Ethnicity affects relapse-free survival in immune-mediated thrombotic thrombocytopenic purpura.
Júlia Weisinger, Florian Blanchard, Benoit Suzon, Christophe Deligny, Jehane Fadlallah, François Provôt, Pascale Poullin, Manon Marie, David Ribes, Gabriel Choukroun, Yahsou Delmas, Elie Azoulay, Ygal Benhamou, Maximilien Grall, Jean-Michel Halimi
Published: 202610.3324/haematol.2025.288789
Abstract
Immune-mediated thrombotic thrombocytopenic purpura (iTTP) is caused by a severe, antibody-mediated deficiency of ADAMTS13 (A Disintegrin And Metalloproteinase with ThromboSpondin-1 motifs, 13th member) activity. The B-cell depleting agent rituximab…
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