Haemophagocytic lymphohistiocytosis and abdominal compartment syndrome in acute pancreatitis.

Haemophagocytic lymphohistiocytosis (HLH) is a rare and often fatal syndrome that may be primary or secondary. This is a case of HLH associated with necrotizing pancreatitis, complicated by abdominal compartment syndrome. It highlights the need for high degree of suspicion for diagnosis in surgical patients, the complexity of managing the sequalae of HLH, and the importance of early treatment.