Respiratory investigationHumansMaleMiddle AgedFemaleAlveolitis
Familial fibrotic hypersensitivity pneumonitis: A distinct clinical phenotype with shorter leukocyte telomere length.
Masashi Nishimura, Hideya Kitamura, Yoichi Tagami, Kazushi Fujimoto, Takashi Fukushima, Ryota Otoshi, Takashi Niwa, Jun Aoki, Taiki Fukuda, Tomoe Sawazumi, Tae Iwasawa, Koji Okudela, Tamiko Takemura, Yayoi Natsume-Kitatani, Yu Hara
Published: 202510.1016/j.resinv.2025.10.012
Abstract
BACKGROUND: Family history is an important factor in recognizing the prognosis of interstitial lung disease (ILD), however, its significance in fibrotic hypersensitivity pneumonitis (HP), as based on the latest international guidelines, remains uncle…
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