Revista espanola de cardiologia (English ed.)
Predictors of poor prognosis in a large cohort of patients with hereditary cardiac transthyretin amyloidosis.
Tomás Ripoll-Vera, Fernando de Frutos, José González-Costello, Ana José Manovel-Sánchez, Esther Zorio-Grima, M Teresa Bosch-Rovira, José Manuel García-Pinilla, María Robledo-Iñarritu, Javier Limeres-Freire, Ana García-Álvarez, María Gallego-Delgado, María Ángeles Espinosa-Castro, José López-Aguilera, Rosa Macías-Ruiz, María Valverde-Gómez
Published: 202510.1016/j.rec.2025.12.016
Abstract
INTRODUCTION AND OBJECTIVES: Hereditary transthyretin amyloidosis (hATTR) is a rare, multisystemic, autosomal dominant disease. Cardiac involvement worsens prognosis. We aimed to characterize Spanish patients with hATTR cardiac amyloidosis (hATTR-CA)…
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