Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society
Improved ventilation inhomogeneity and lower LCI variability under ETI: Retrospective analysis in a pediatric cohort.
Tabitha Arn-Roth, Tessa Bernasconi, Bettina Sarah Frauchiger, Insa Korten, Carmen Casaulta, Elisabeth Kieninger, Philipp Latzin
Published: 202510.1016/j.jcf.2025.12.016
Abstract
BACKGROUND: Elexacaftor/tezacaftor/ivacaftor (ETI) has transformed cystic fibrosis (CF) therapy, yet observational clinical data in children with preserved spirometry remain limited. The lung clearance index (LCI) is used to monitor treatment respons…
Preview only. Read the full abstract at the source